Трансплантация сердца ребенку после операции Фонтена

Операция «Fontan» является одним из методов гемодинамической коррекции сложных врожденных пороков сердца, когда невозможно выполнить радикальную коррекцию в связи с анатомическими особенностями порока. В отдаленном периоде от 10 до 20 лет развиваются проявления сердечной недостаточности с формированием симптомокомплекса Failing Fontan, требующего коррекции медикаментозной терапии, и возможно использование хирургических методик, включая трансплантацию сердца. Зарубежными иссле- дованиями показано, что трансплантация является эффективным методом сохранения жизни реципиента и стабилизации его состояния. В статье представлен первый опыт трансплантации сердца ребенку после операции Фонтена в Российской Федерации.

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