vtioВестник трансплантологии и искусственных органовRussian Journal of Transplantology and Artificial Organs1995-1191Academician V.I.Shumakov National Medical Research Center of Transplantology and Artificial Organs", Ministry of Health of the Russian Federation10.15825/1995-1191-2025-2-60-68vtio-1920Research ArticleТрансплантация сердца и вспомогательное кровообращениеHeart Transplantation and Assisted CirculationТрансплантация сердца ребенку после операции ФонтенаPediatric heart transplantation after a Fontan procedureРябцевД. В.RyabtsevD. V.

Москва

Moscow

ИвановА. С.IvanovA. S.

Москва

Moscow

БековМ. Т.BekovM. T.

Москва

Moscow

СпиринаЕ. А.SpirinaE. A.

Москва

Moscow

ПопцовВ. Н.PoptsovV. N.

Москва

Moscow

КавардаковаЕ. С.KavardakovaE. S.

Москва

Moscow

https://orcid.org/0009-0003-3622-767XЧартаевА. Ч.ChartaevA. Ch.

Чартаев Абулмуслим Чартаевич

123182, Москва, ул. Щукинская, д. 1

Abulmuslim Ch. Chartaev

1, Shchukinskaya str., Moscow, 123182

ГотьеС. В.GautierS. V.

Москва

Moscow

ФГБУ «Национальный медицинский исследовательский центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава РоссииРоссияShumakov National Medical Research Center of Transplantology and Artificial OrgansRussian FederationФГБУ «Национальный медицинский исследовательский центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава России; ФГАОУ ВО Первый Московский государственный медицинский университет имени И.М. Сеченова Минздрава России (Сеченовский университет),РоссияShumakov National Medical Research Center of Transplantology and Artificial Organs; Sechenov UniversityRussian Federation2025120720252726068Copyright © Рябцев Д.В., Иванов А.С., Беков М.Т., Спирина Е.А., Попцов В.Н., Кавардакова Е.С., Чартаев А.Ч., Готье С.В., 20252025Рябцев Д.В., Иванов А.С., Беков М.Т., Спирина Е.А., Попцов В.Н., Кавардакова Е.С., Чартаев А.Ч., Готье С.В.Ryabtsev D.V., Ivanov A.S., Bekov M.T., Spirina E.A., Poptsov V.N., Kavardakova E.S., Chartaev A.C., Gautier S.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.transpl.ru/vtio/article/view/1920

Операция «Fontan» является одним из методов гемодинамической коррекции сложных врожденных пороков сердца, когда невозможно выполнить радикальную коррекцию в связи с анатомическими особенностями порока. В отдаленном периоде от 10 до 20 лет развиваются проявления сердечной недостаточности с формированием симптомокомплекса Failing Fontan, требующего коррекции медикаментозной терапии, и возможно использование хирургических методик, включая трансплантацию сердца. Зарубежными иссле- дованиями показано, что трансплантация является эффективным методом сохранения жизни реципиента и стабилизации его состояния. В статье представлен первый опыт трансплантации сердца ребенку после операции Фонтена в Российской Федерации.

The Fontan procedure is a surgical technique used for hemodynamic correction of complex congenital heart defects (CHDs), and is used when radical correction of CHDs is anatomically impossible. In the long term – from 10 to 20 years – Fontan circulation can lead to «failing Fontan» characterized by heart failure symptoms, requiring adjustments to medical treatment and potentially surgical interventions, including heart transplantation (HT). Foreign studies indicate that HT is an effective method for prolonging life in patients with failing Fontan circulation. It stabilizes the patient’s condition. This paper presents the first documented case of HT in a child following a Fontan procedure in the Russian Federation.

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The authors declare that there are no conflicts of interest present.