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Вестник трансплантологии и искусственных органов

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Способы лечения гипертрофической кардиомиопатии в зависимости от ее анатомического варианта

https://doi.org/10.15825/1995-1191-2026-1-85-97

Аннотация

Гипертрофическая кардиомиопатия (ГКМП) – это наиболее частое наследственное заболевание серд ца, которое отличается разнообразием проявлений: от морфологических особенностей и течения болезни до клинической картины и гемодинамических параметров. Стратегия лечения ГКМП должна быть строго персонализированной и учитывать не только гемодинамические параметры, но и анатомические особенности. Классификация ГКМП на основе наличия или отсутствия обструкции выводного отдела левого желудочка, а также локализации гипертрофии межжелудочковой перегородки (базальный, срединный и апикальный типы) диктуют выбор оптимальной стратегии ведения пациентов. Медикаментозная терапия, хирургическая миэктомия или спиртовая септальная абляция являются основными методами лечения обструктивной ГКМП, в то время как при необструктивной форме акцент делается на контроле симптомов и профилактике осложнений. Учитывая риск внезапной сердечной смерти, особое внимание следует уделять своевременной имплантации кардиовертера-дефибриллятора пациентам с высоким риском.

Об авторах

Ю. В. Семенова
ФГБУ «Национальный медицинский исследовательский центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава России
Россия

Семенова Юлия Викторовна

123182, Москва, ул. Щукинская, д. 1. Тел. (985) 250-72-82



Б. Л. Миронков
ФГБУ «Национальный медицинский исследовательский центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава России
Россия

Москва,



Д. А. Изотов
ФГБУ «Национальный медицинский исследовательский центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава России
Россия

Москва,



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Семенова Ю.В., Миронков Б.Л., Изотов Д.А. Способы лечения гипертрофической кардиомиопатии в зависимости от ее анатомического варианта. Вестник трансплантологии и искусственных органов. 2026;28(1):85-97. https://doi.org/10.15825/1995-1191-2026-1-85-97

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Semenova Yu.V., Mironkov B.L., Izotov D.A. Treatment strategies for hypertrophic cardiomyopathy based on anatomical variant. Russian Journal of Transplantology and Artificial Organs. 2026;28(1):85-97. (In Russ.) https://doi.org/10.15825/1995-1191-2026-1-85-97

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ISSN 1995-1191 (Print)