Pediatric heart transplantation after a Fontan procedure
D. V. Ryabtsev,
A. S. Ivanov,
M. T. Bekov,
E. A. Spirina,
V. N. Poptsov,
E. S. Kavardakova, 
A. C. Chartaev,
S. V. Gautier
A. C. Chartaev,
S. V. Gautier https://doi.org/10.15825/1995-1191-2025-2-60-68
Abstract
The Fontan procedure is a surgical technique used for hemodynamic correction of complex congenital heart defects (CHDs), and is used when radical correction of CHDs is anatomically impossible. In the long term – from 10 to 20 years – Fontan circulation can lead to «failing Fontan» characterized by heart failure symptoms, requiring adjustments to medical treatment and potentially surgical interventions, including heart transplantation (HT). Foreign studies indicate that HT is an effective method for prolonging life in patients with failing Fontan circulation. It stabilizes the patient’s condition. This paper presents the first documented case of HT in a child following a Fontan procedure in the Russian Federation.
About the Authors
D. V. Ryabtsev
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Moscow
A. S. Ivanov
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Moscow
M. T. Bekov
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Moscow
E. A. Spirina
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Moscow
V. N. Poptsov
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Moscow
E. S. Kavardakova
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Moscow
A. C. Chartaev
Shumakov National Medical Research Center of Transplantology and Artificial Organs
Russian Federation
Russian Federation
Abulmuslim C. Chartaev
1, Shchukinskaya str., Moscow, 123182
S. V. Gautier
Shumakov National Medical Research Center of Transplantology and Artificial Organs;
Sechenov University
Russian Federation
Russian Federation
Moscow
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For citations:
Ryabtsev D.V., Ivanov A.S., Bekov M.T., Spirina E.A., Poptsov V.N., Kavardakova E.S., Chartaev A.C., Gautier S.V. Pediatric heart transplantation after a Fontan procedure. Russian Journal of Transplantology and Artificial Organs. 2025;27(2):60-68. (In Russ.) https://doi.org/10.15825/1995-1191-2025-2-60-68
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