vtioВестник трансплантологии и искусственных органовRussian Journal of Transplantology and Artificial Organs1995-1191Academician V.I.Shumakov National Medical Research Center of Transplantology and Artificial Organs", Ministry of Health of the Russian Federation10.15825/1995-1191-2016-4-146-156vtio-709Research ArticleОбзор литературыLiterature ReviewsНЕКОМПАКТНАЯ КАРДИОМИОПАТИЯNONCOMPACTION CARDIOMYOPATHYИльинскийИ. М.IljinskyI. M.

Кафедра трансплантологии и искусственных органов ГБОУ ВПО «Первый Московскийгосударственный медицинский университет имени И.М. Сеченова» Минздрава России

Адрес: 123182, Москва, ул. Щукинская, д. 1. Тел. (926) 811-84-55

I.M. Sechenov First Moscow State Medical University, Department of transplantology and artifi cial organs, Moscow, Russian Federation

iiljinsky@mail.ruМожейкоН. П.MozheykoN. P.

Москва, Российская Федерация

ШевченкоА. О.ShevchenkoA. O.

Кафедра трансплантологии и искусственных органов ГБОУ ВПО «Первый Московскийгосударственный медицинский университет имени И.М. Сеченова» Минздрава России, Москва, Российская Федерация

I.M. Sechenov First Moscow State Medical University, Department of transplantology and artifi cial organs, Moscow, Russian Federation

ФГБУ «Федеральный научный центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава России ГБОУ ВПО «Первый Московский государственный медицинский университет имени И.М. Сеченова» Минздрава РоссииРоссияV.I. Shumakov Federal Research Center of Transplantology and Artificial Organs of the Ministry of Healthcare of the Russian Federation I.M. Sechenov First Moscow State Medical UniversityRussian FederationФГБУ «Федеральный научный центр трансплантологии и искусственных органов имени академика В.И. Шумакова» Минздрава РоссииРоссияV.I. Shumakov Federal Research Center of Transplantology and Artificial Organs of the Ministry of Healthcare of the Russian FederationRussian Federation201628012017184146156Copyright © Ильинский И.М., Можейко Н.П., Шевченко А.О., 20172017Ильинский И.М., Можейко Н.П., Шевченко А.О.Iljinsky I.M., Mozheyko N.P., Shevchenko A.O.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.transpl.ru/vtio/article/view/709

В статье представлен обзор литературы по различным аспектам некомпактной кардиомиопатии. Некомпактная кардиомиопатия – относительно редкое врожденное заболевание сердца, характеризующееся чрезмерным развитием трабекулярной сети и глубокими межтрабекулярными впадинами миокарда желудочков. Наиболее часто встречается неуплотненный миокард левого желудочка (НМЛЖ). НМЛЖ может быть изолированным или сосуществовать с другими кардиальными и системными аномалиями. Неуплотнение диагностируют, используя эхокардиографию или магнитно-резонансную томографию. Клинические проявления варьируют в широких пределах – от бессимптомных пациентов до пациентов с желудочковыми аритмиями, застойной сердечной недостаточностью и тромбоэмболиями. Некомпактный миокард является нерешенной клинической задачей в силу недостаточной точности неинвазивной диагностики и стратификации пациентов, определения прогноза и в ряде случаев – тактики их лечения.

In this article, the review of the literature on various aspects of the noncompaction cardiomyopathy is presented. Non-compaction cardiomyopathy is a relatively rare congenital heart disease characterized by an excessive prominence of trabecular meshwork, and deep recesses of the ventricular myocardium. The most frequent is left ventricular noncompaction (LVNC). LVNC can occur in isolation or coexist with other cardiac and systemic anomalies. Noncompaction can be detected with an echocardiography or cardiac magnetic resonance imaging. The clinical presentation varies ranging from asymptomatic patients to patients who develop ventricular arrhythmias, heart failure, thromboembolism.

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The authors declare that there are no conflicts of interest present.